NUMERO: #20230251

Título: HEREDITARY HEMORRHAGIC TELANGIECTASIA IN MUCOSA AND FACE

Nome do Apresentador: Rubens Signoretti Oliveira SILVA

Categoria do Trabalho: Painel de caso clínico (PCC)

Área Temática: Estomatologia

Resumo: Hereditary Hemorrhagic Telangiectasia (HHT), also known as Rendu-Osler-Weber syndrome, is a rare autosomal dominant disease. This condition is characterized by the presence of mucosal, visceral, and dermal telangiectasias. The present study reports a case of a 68-year-old individual diagnosed with HHT since 2007. The patient reports a progressive occurrence of telangiectasias on the face, oral mucosa, lips, palate, and tongue. In 2014 and 2018, the patient developed a cerebral abscess 15 days after dental manipulation for endodontic treatment. The patient also had episodes of epistaxis and gingival bleeding and underwent sessions of vascular sclerotherapy on the oral mucosa under antibiotic prophylaxis. In 2022, the patient presented with hypovolemic shock requiring volume resuscitation due to recurrent epistaxis and gingival bleeding. After recovery, new sclerotherapy sessions were performed. The patient is under follow-up with a proposal for new sclerotherapy sessions, without recent episodes of bleeding of buccal origin.

Autor 1:  Rubens Signoretti Oliveira SILVA

E-mail 1:  [email protected]

Autor 2:   Sicília Rezende Oliveira

E-mail 2:  [email protected]

Autor 3 :  Paula Alves da Silva Rocha

E-mail 3:  [email protected]

Autor 4:  Nayara Conceição Marcos Santana

E-mail 4:  [email protected]

Autor 5:  Vanessa Fátima Bernardes

E-mail 5:  [email protected]

Autor 6:  Ricardo Alves de Mesquita

E-mail 6:  [email protected]

Autor 7:  Tarcília Aparecida da Silva

E-mail 7:  [email protected]