NUMERO: #20230016

Título: OSTEOMA AND DESMOID TUMOR AS FIRST CLINICAL SIGN OF GARDNER SYNDROME: A REPORT OF TWO CASES

Nome do Apresentador: Clara Herrera FREIRE

Categoria do Trabalho: Painel de caso clínico (PCC)

Área Temática: Estomatologia

Resumo: Gardner syndrome (GS) is a genetic disorder characterized by intestinal polyps, osteomas, and soft-tissue tumors. This study aimed to describe two patients with GS. An 11-year-old female presented with a giant osteoma in the left mandible and a desmoid tumor in the right mandible. During the anamnesis, it was reported that two aunts of the patient died with colorectal cancer. Her cousin, a 20-year-old male presented with multiple osteomas in the maxilla and mandible. Since both patient were suspected to have GS, gastrointestinal endoscopic was performed and revealed multiple polyposis. The final diagnosis was GS. Osteoma and desmoid tumor may be an important indicator of GS, and should guide dentists to perform clinical investigations in order to confirm or exclude GS.

Autor 1:  Clara Herrera FREIRE

E-mail 1:  [email protected]

Autor 2:   Israel Leal Cavalcante

E-mail 2:  [email protected]

Autor 3 :  José Victor Lemos Ventura

E-mail 3:  [email protected]

Autor 4:  John Lennon Silva Cunha

E-mail 4:  [email protected]

Autor 5:  Jefferson da Rocha Tenório

E-mail 5:  [email protected]

Autor 6:  Ana Maria Calderoni

E-mail 6:  [email protected]

Autor 7:  Bruno Augusto Benevenuto de Andrade

E-mail 7:  [email protected]